A rare and unusual presentation of aplasia cutis congenita | Article

for neonatal and paediatric healthcare professionals

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Keywords

aplasia cutis congenita; skin disorder; congenital; placental infarct; fetus papyraceus

Key points

Extensive ACC lesions on the trunk and limbs are rare.
ACC can be associated with placental infarcts or the in utero death of a twin fetus, as in the case presented here.
Obstetric history should review maternal medications/infections during pregnancy, determine an initial multiple pregnancy with death of a co-twin and investigate any placental anomalies.
Despite their large size, truncal and limb ACC lesions usually resolve within the first few months of life.

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VOLUME 15/ISSUE 5, SEPTEMBER 2019

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